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ETMR-10. EARLY FOCAL RADIOTHERAPY AND TEMOZOLOMIDE FOLLOWING COMPLETE RESECTION APPEAR SUPERIOR TO INTENSIVE CHEMOTHERAPY AND DELAYED RADIOTHERAPY IN CHILDREN WITH EMBRYONAL TUMORS WITH MULTILAYERED ROSETTES (ETMR)

BACKGROUND: Embryonal tumor with multilayered rosettes (ETMR) is a rare, aggressive embryonal central nervous system tumor characterized by LIN28A expression and alterations in the C19MC locus. ETMRs predominantly occur in young children, have a dismal prognosis, and no definitive treatment guidelin...

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Опубликовано в: :Neuro Oncol
Главные авторы: Mayr, Lisa, Gojo, Johannes, Peyrl, Andreas, Azizi, Amedeo, Dieckmann, Karin, Haberler, Christine, Czech, Thomas, Slavc, Irene
Формат: Artigo
Язык:Inglês
Опубликовано: Oxford University Press 2020
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7715625/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/neuonc/noaa222.214
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