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RARE-12. EARLY FOCAL RADIOTHERAPY AND TEMOZOLOMIDE FOLLOWING COMPLETE RESECTION APPEAR SUPERIOR TO INTENSIVE CHEMOTHERAPY IN CHILDREN WITH EMBRYONAL TUMORS WITH MULTILAYERED ROSETTES (ETMR)

BACKGROUND: Embryonal tumor with multilayered rosettes (ETMR) is an extremely rare entity characterized by LIN28A expression and alterations in the C19MC locus. ETMRs predominantly occur in young children and have a dismal prognosis. We report on our single institution experience in seven consecutiv...

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Publicat a:Neuro Oncol
Autors principals: Slavc, Irene, Mayr, Lisa, Gojo, Johannes, Peyrl, Andreas, Azizi, Amedeo, Dieckmann, Karin, Haberler, Christine, Czech, Thomas
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2019
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6847062/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/neuonc/noz175.935
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