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Novel Variant of AVPR2 Giving Rise to X-Linked Congenital Nephrogenic Diabetes Insipidus in a 7-Month-Old Danish Boy

Patients affected with congenital nephrogenic diabetes insipidus (CNDI) have reduced ability to concentrate urine. Early diagnosis of CNDI is important to avoid recurrent episodes of severe dehydration. We present a Danish male suffering from typical symptoms and diagnosed with CNDI at the age of 7...

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Detalhes bibliográficos
Publicado no:Case Rep Nephrol Dial
Main Authors: Sollid, Johanne Emy, Joshi, Shivani, Pulczynska Wason, Malgorzata, Rittig, Søren, Hvarregaard Christensen, Jane, Kamperis, Konstantinos
Formato: Artigo
Idioma:Inglês
Publicado em: S. Karger AG 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7670377/
https://ncbi.nlm.nih.gov/pubmed/33251249
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000508786
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