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Mouse models to study the pathophysiology of combined methylmalonic acidemia and homocystinuria, cblC type

Combined methylmalonic acidemia and homocystinuria, cblC type, is the most common inherited disorder of cobalamin metabolism and is characterized by severe fetal developmental defects primarily impacting the central nervous system, hematopoietic system, and heart. CblC was previously shown to be due...

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Dettagli Bibliografici
Pubblicato in:Dev Biol
Autori principali: Chern, Tiffany, Achilleos, Annita, Tong, Xuefei, Hsu, Chih-Wei, Wong, Leeyean, Poché, Ross A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2020
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7669717/
https://ncbi.nlm.nih.gov/pubmed/32941884
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ydbio.2020.09.005
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