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Hereditary Hypofibrinogenemia with Hepatic Storage
Fibrinogen is a 340-kDa plasma glycoprotein constituted by two sets of symmetrical trimers, each formed by the Aα, Bβ, and γ chains (respectively coded by the FGA, FGB, and FGG genes). Quantitative fibrinogen deficiencies (hypofibrinogenemia, afibrinogenemia) are rare congenital disorders characteri...
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| Publicado en: | Int J Mol Sci |
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| Autores principales: | , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
MDPI
2020
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7659954/ https://ncbi.nlm.nih.gov/pubmed/33105716 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21217830 |
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