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Glued in lipids: Lipointoxication in cystic fibrosis

Cystic Fibrosis (CF) is an autosomal recessive disease caused by mutations in the CF transmembrane regulator (CFTR) gene, which encodes a chloride channel located at the apical surface of epithelial cells. Unsaturated Fatty Acid (UFA) deficiency has been a persistent observation in tissues from pati...

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Dettagli Bibliografici
Pubblicato in:EBioMedicine
Autori principali: Vandebrouck, Clarisse, Ferreira, Thierry
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7648119/
https://ncbi.nlm.nih.gov/pubmed/33038767
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ebiom.2020.103038
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