A carregar...

Mutant MESD links cellular stress to type I collagen aggregation in osteogenesis imperfecta type XX

Aberrant forms of endoplasmic reticulum (ER)-resident chaperones are implicated in loss of protein quality control in rare diseases. Here we report a novel mutation (p.Asp233Asn) in the ER retention signal of MESD by whole exome sequencing of an individual diagnosed with osteogenesis imperfecta (OI)...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Matrix Biol
Main Authors: Ghosh, Debasish Kumar, Udupa, Prajna, Shrikondawar, Akshaykumar Nanaji, Bhavani, Gandham SriLakshmi, Shah, Hitesh, Ranjan, Akash, Girisha, Katta M.
Formato: Artigo
Idioma:Inglês
Publicado em: 2023
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7615836/
https://ncbi.nlm.nih.gov/pubmed/36526215
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.matbio.2022.12.001
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!