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Pleuroparenchymal fibroelastosis in systemic sclerosis: prevalence and prognostic impact

Interstitial lung disease (ILD) in systemic sclerosis (SSc) is a major cause of morbidity and mortality, mostly presenting as nonspecific interstitial pneumonia. Little is known about the prevalence of pleuroparenchymal fibroelastosis (PPFE), a specific entity affecting the visceral pleura and subpl...

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Publicat a:Eur Respir J
Autors principals: Bonifazi, Martina, Sverzellati, Nicola, Negri, Eva, Jacob, Joseph, Egashira, Ryoko, Moser, Joanna, Piciucchi, Sara, Mei, Federico, De Lauretis, Angelo, Visca, Dina, Goh, Nicole, Bonini, Matteo, Cirilli, Laura, LaVecchia, Carlo, Chua, Felix, Kouranos, Vasileios, Margaritopoulos, George, Kokosi, Maria, Maher, Toby M, Gasparini, Stefano, Gabrielli, Armando, Wells, Athol U, Renzoni, Elisabetta A
Format: Artigo
Idioma:Inglês
Publicat: 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7615192/
https://ncbi.nlm.nih.gov/pubmed/32299855
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/13993003.02135-2019
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