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Pleuroparenchymal Fibroelastosis. A Review of Clinical, Radiological, and Pathological Characteristics

Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique clinical, radiological, and pathological characteristics. Designated a rare idiopathic interstitial pneumonia in 2013, its name refers to a combination of fibrosis involving the visceral pleura and fibroelastotic cha...

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Detalhes bibliográficos
Publicado no:Ann Am Thorac Soc
Main Authors: Chua, Felix, Desai, Sujal R., Nicholson, Andrew G., Devaraj, Anand, Renzoni, Elisabetta, Rice, Alexandra, Wells, Athol U.
Formato: Artigo
Idioma:Inglês
Publicado em: American Thoracic Society 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6945468/
https://ncbi.nlm.nih.gov/pubmed/31425665
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/AnnalsATS.201902-181CME
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