A carregar...

Cardiomyopathy and altered integrin-actin signaling in Fhl1 mutant female mice

X-linked scapuloperoneal myopathy (X-SM), one of Four-and-a-half LIM 1 (FHL1) related diseases, is an adult-onset slowly progressive myopathy, often associated with cardiomyopathy. We previously generated a knock-in mouse model that has the same mutation (c.365 G > C, p.W122S) as human X-SM patie...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Hum Mol Genet
Main Authors: Kubota, Akatsuki, Juanola-Falgarona, Martí, Emmanuele, Valentina, Sanchez-Quintero, Maria Jose, Kariya, Shingo, Sera, Fusako, Homma, Shunichi, Tanji, Kurenai, Quinzii, Catarina M, Hirano, Michio
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7594173/
https://ncbi.nlm.nih.gov/pubmed/30260394
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddy299
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!