Cargando...

Structural and Functional Brain Abnormalities in Mouse Models of Lafora Disease

Mutations in the EPM2A and EPM2B genes, encoding laforin and malin proteins respectively, are responsible for Lafora disease, a fatal form of progressive myoclonus epilepsy with autosomal recessive inheritance. Neuroimaging studies of patients with Lafora disease have shown different degrees of brai...

Descripción completa

Guardado en:
Detalles Bibliográficos
Publicado en:Int J Mol Sci
Autores principales: Burgos, Daniel F., Cussó, Lorena, Sánchez-Elexpuru, Gentzane, Calle, Daniel, Perpinyà, Max Bautista, Desco, Manuel, Serratosa, José M., Sánchez, Marina P.
Formato: Artigo
Lenguaje:Inglês
Publicado: MDPI 2020
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7589150/
https://ncbi.nlm.nih.gov/pubmed/33092303
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21207771
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!