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Sodium selenate treatment improves symptoms and seizure susceptibility in a malin-deficient mouse model of Lafora disease

OBJECTIVE: To search for new therapies aimed at ameliorating the neurologic symptoms and epilepsy developing in patients with Lafora disease. METHODS: Lafora disease is caused by loss-of-function mutations in either the EPM2A or EPM2B genes. Epm2a(−/−) and Epm2b(−/−) mice display neurologic and beha...

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Detalhes bibliográficos
Publicado no:Epilepsia
Main Authors: Sánchez-Elexpuru, Gentzane, Serratosa, José M., Sánchez, Marina P.
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5495962/
https://ncbi.nlm.nih.gov/pubmed/28098937
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/epi.13656
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