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Changes in expressions of genes involved in the regulation of cellular processes in mucopolysaccharidoses as assessed by fibroblast culture-based transcriptomic analyses

Recent studies indicated that apart from lysosomal storage of glycosaminoglycans (GAGs), secondary and tertiary changes in cellular processes may significantly contribute to development of disorders and symptoms occurring in mucopolysaccharidoses (MPS), a group of lysosomal storage diseases in which...

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Опубликовано в: :Metab Brain Dis
Главные авторы: Gaffke, Lidia, Pierzynowska, Karolina, Krzelowska, Karolina, Piotrowska, Ewa, Węgrzyn, Grzegorz
Формат: Artigo
Язык:Inglês
Опубликовано: Springer US 2020
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7584551/
https://ncbi.nlm.nih.gov/pubmed/32886284
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11011-020-00614-2
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