Spontaneous Right Ventricular Pseudoaneurysms and Increased Arrhythmogenicity in a Mouse Model of Marfan Syndrome

Patients with Marfan syndrome (MFS), a connective tissue disorder caused by pathogenic variants in the gene encoding the extracellular matrix protein fibrillin-1, have an increased prevalence of primary cardiomyopathy, arrhythmias, and sudden cardiac death. We have performed an in-depth in vivo and...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Int J Mol Sci
Prif Awduron: Steijns, Felke, Renard, Marjolijn, Vanhomwegen, Marine, Vermassen, Petra, Desloovere, Jana, Raedt, Robrecht, Larsen, Lars E., Tóth, Máté I., De Backer, Julie, Sips, Patrick
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: MDPI 2020
Pynciau:
Article
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC7582482/
https://ncbi.nlm.nih.gov/pubmed/32987703
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21197024
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