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Moyamoya and progressive myoclonic epilepsy secondary to CLN6 bi-allelic mutations – A previously unreported association

The neuronal ceroid lipofuscinoses (NCL) are a collection of lysosomal storage diseases characterised by the accumulation of characteristic inclusions containing lipofuscin in various tissues of the body and are one of the causes of progressive myoclonic epilepsy. Mutations in at least thirteen gene...

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Dettagli Bibliografici
Pubblicato in:Epilepsy Behav Rep
Autori principali: Talbot, Jamie, Singh, Priyanka, Puvirajasinghe, Clinda, Sisodiya, Sanjay M., Rugg-Gunn, Fergus
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7528204/
https://ncbi.nlm.nih.gov/pubmed/33024953
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ebr.2020.100389
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