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Pulmonary capillary hemangiomatosis-predominant vasculopathy in a patient with rheumatoid arthritis-associated interstitial lung disease: An autopsy report

Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension (PH) associated with poor prognosis. Clinically, it is characterized by severe hypoxemia, centrilobular ground-glass opacities on computed tomography, and pulmonary congestion triggered by pulmonary vasodilating ther...

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Detalhes bibliográficos
Publicado no:Respir Med Case Rep
Main Authors: Nakamura, Junichi, Tsujino, Ichizo, Yamamoto, Gaku, Nakaya, Toshitaka, Takahashi, Kei, Kimura, Hirokazu, Sato, Takahiro, Watanabe, Taku, Nakagawa, Shimpei, Otsuka, Noriyuki, Ohira, Hiroshi, Konno, Satoshi
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7527749/
https://ncbi.nlm.nih.gov/pubmed/33024689
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2020.101215
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