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Fanconi–Bickel syndrome in a Ugandan child – diagnostic challenges in resource-limited settings: a case report

BACKGROUND: Fanconi–Bickel syndrome is an autosomal recessive disorder of glucose metabolism. It is an extremely rare disorder. Most cases have been reported in consanguineous communities. None of the cases have been reported in Black Africans in sub-Saharan Africa. This case was diagnosed 3 years a...

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Dades bibliogràfiques
Publicat a:J Med Case Rep
Autors principals: Piloya, Thereza, Ssematala, Hawa, Dramani, Lydia Paparu, Nalikka, Oliva, Baluka, Miriam, Musiime, Victor
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7526154/
https://ncbi.nlm.nih.gov/pubmed/32993803
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13256-020-02488-5
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