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Fanconi–Bickel syndrome in a Ugandan child – diagnostic challenges in resource-limited settings: a case report

BACKGROUND: Fanconi–Bickel syndrome is an autosomal recessive disorder of glucose metabolism. It is an extremely rare disorder. Most cases have been reported in consanguineous communities. None of the cases have been reported in Black Africans in sub-Saharan Africa. This case was diagnosed 3 years a...

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Detalhes bibliográficos
Publicado no:J Med Case Rep
Main Authors: Piloya, Thereza, Ssematala, Hawa, Dramani, Lydia Paparu, Nalikka, Oliva, Baluka, Miriam, Musiime, Victor
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7526154/
https://ncbi.nlm.nih.gov/pubmed/32993803
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13256-020-02488-5
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