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Long-Term Efficacy of Subcutaneous C1 Inhibitor in Pediatric Patients with Hereditary Angioedema

Background: Hereditary angioedema (HAE) due to C1 inhibitor (C1INH) deficiency is characterized by recurrent attacks of edema of the skin and mucosal tissues. Symptoms usually present during childhood (mean age at first attack, 10 years). Earlier symptom onset may predict a more severe disease cours...

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Detaylı Bibliyografya
Yayımlandı:Pediatr Allergy Immunol Pulmonol
Asıl Yazarlar: Levy, Donald, Caballero, Teresa, Hussain, Iftikhar, Reshef, Avner, Anderson, John, Baker, James, Schwartz, Lawrence B., Cicardi, Marco, Prusty, Subhransu, Feuersenger, Henrike, Pragst, Ingo, Manning, Michael E.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Mary Ann Liebert, Inc., publishers 2020
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC7499895/
https://ncbi.nlm.nih.gov/pubmed/32953229
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1089/ped.2020.1143
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