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Comparison of Multiple Breath Washout and Spirometry in Children with Primary Ciliary Dyskinesia and Cystic Fibrosis and Healthy Controls

Rationale: In cystic fibrosis (CF), the lung clearance index (LCI), derived from multiple breath washout (MBW), is more sensitive in detecting early lung disease than FEV(1); MBW has been less thoroughly evaluated in young patients with primary ciliary dyskinesia (PCD). Objectives: Our objectives we...

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Bibliografske podrobnosti
izdano v:Ann Am Thorac Soc
Main Authors: Kinghorn, BreAnna, McNamara, Sharon, Genatossio, Alan, Sullivan, Erin, Siegel, Molly, Bauer, Irma, Clem, Charles, Johnson, Robin C., Davis, Miriam, Griffiths, Anne, Wheeler, William, Johnson, Katherine, Davis, Stephanie D., Leigh, Margaret W., Rosenfeld, Margaret, Pittman, Jessica
Format: Artigo
Jezik:Inglês
Izdano: American Thoracic Society 2020
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC7462330/
https://ncbi.nlm.nih.gov/pubmed/32603187
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/AnnalsATS.201905-375OC
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