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POT1 mutation spectrum in tumor types commonly diagnosed among POT1-associated hereditary cancer syndrome families

BACKGROUND: The shelterin complex is composed of six proteins that protect and regulate telomere length, including protection of telomeres 1 (POT1). Germline POT1 mutations are associated with an autosomal dominant familial cancer syndrome presenting with diverse malignancies including glioma, angio...

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Dades bibliogràfiques
Publicat a:J Med Genet
Autors principals: Shen, Erica, Xiu, Joanne, López, Giselle Y., Bentley, Rex, Jalali, Ali, Heimberger, Amy B., Bainbridge, Matthew N., Bondy, Melissa L., Walsh, Kyle M.
Format: Artigo
Idioma:Inglês
Publicat: 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7427478/
https://ncbi.nlm.nih.gov/pubmed/31937561
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/jmedgenet-2019-106657
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