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Newborn Screening for Pompe Disease

Glycogen storage disease type II (also known as Pompe disease (PD)) is an autosomal recessive disorder caused by defects in α-glucosidase (AαGlu), resulting in lysosomal glycogen accumulation in skeletal and heart muscles. Accumulation and tissue damage rates depend on residual enzyme activity. Enzy...

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Détails bibliographiques
Publié dans:Int J Neonatal Screen
Auteurs principaux: Sawada, Takaaki, Kido, Jun, Nakamura, Kimitoshi
Format: Artigo
Langue:Inglês
Publié: MDPI 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7423004/
https://ncbi.nlm.nih.gov/pubmed/33073027
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijns6020031
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