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Adenosine deaminase 2 as a biomarker of macrophage activation syndrome in systemic juvenile idiopathic arthritis

OBJECTIVE: Macrophage activation syndrome (MAS) is a life-threatening complication of systemic juvenile idiopathic arthritis (sJIA) characterized by a vicious cycle of immune amplification that can culminate in overwhelming inflammation and multi-organ failure. The clinical features of MAS overlap w...

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Pubblicato in:Ann Rheum Dis
Autori principali: Lee, Pui Y., Schulert, Grant S., Canna, Scott W., Huang, Yuelong, Sundel, Jacob, Li, Ying, Hoyt, Kacie J., Blaustein, Rachel B., Wactor, Alexandra, Do, Thuy, Halyabar, Olha, Chang, Margaret H., Dedeoglu, Fatma, Case, Siobhan M., Meidan, Esra, Lo, Mindy S., Sundel, Robert P., Richardson, Edward T., Newburger, Jane W., Hershfield, Michael S., Son, Mary Beth, Henderson, Lauren A., Nigrovic, Peter A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7385992/
https://ncbi.nlm.nih.gov/pubmed/31707357
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/annrheumdis-2019-216030
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