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A Crucial Role for the Protein Quality Control System in Motor Neuron Diseases

Motor neuron diseases (MNDs) are fatal diseases characterized by loss of motor neurons in the brain cortex, in the bulbar region, and/or in the anterior horns of the spinal cord. While generally sporadic, inherited forms linked to mutant genes encoding altered RNA/protein products have also been des...

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Bibliografiske detaljer
Udgivet i:Front Aging Neurosci
Main Authors: Cristofani, Riccardo, Crippa, Valeria, Cicardi, Maria Elena, Tedesco, Barbara, Ferrari, Veronica, Chierichetti, Marta, Casarotto, Elena, Piccolella, Margherita, Messi, Elio, Galbiati, Mariarita, Rusmini, Paola, Poletti, Angelo
Format: Artigo
Sprog:Inglês
Udgivet: Frontiers Media S.A. 2020
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC7385251/
https://ncbi.nlm.nih.gov/pubmed/32792938
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnagi.2020.00191
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