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The Regulation of the Small Heat Shock Protein B8 in Misfolding Protein Diseases Causing Motoneuronal and Muscle Cell Death

Misfolding protein diseases are a wide class of disorders in which the aberrantly folded protein aggregates accumulate in affected cells. In the brain and in the skeletal muscle, misfolded protein accumulation induces a variety of cell dysfunctions that frequently lead to cell death. In motoneuron d...

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Detalhes bibliográficos
Publicado no:Front Neurosci
Main Authors: Cristofani, Riccardo, Rusmini, Paola, Galbiati, Mariarita, Cicardi, Maria Elena, Ferrari, Veronica, Tedesco, Barbara, Casarotto, Elena, Chierichetti, Marta, Messi, Elio, Piccolella, Margherita, Carra, Serena, Crippa, Valeria, Poletti, Angelo
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6688727/
https://ncbi.nlm.nih.gov/pubmed/31427919
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnins.2019.00796
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