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Dietary lipids in glycogen storage disease type III: A systematic literature study, case studies, and future recommendations

A potential role of dietary lipids in the management of hepatic glycogen storage diseases (GSDs) has been proposed, but no consensus on management guidelines exists. The aim of this study was to describe current experiences with dietary lipid manipulations in hepatic GSD patients. An international s...

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Bibliografiset tiedot
Julkaisussa:J Inherit Metab Dis
Päätekijät: Rossi, Alessandro, Hoogeveen, Irene J., Bastek, Vanessa B., de Boer, Foekje, Montanari, Chiara, Meyer, Uta, Maiorana, Arianna, Bordugo, Andrea, Dianin, Alice, Campana, Carmen, Rigoldi, Miriam, Kishnani, Priya S., Pendyal, Surekha, Strisciuglio, Pietro, Gasperini, Serena, Parenti, Giancarlo, Parini, Rossella, Paci, Sabrina, Melis, Daniela, Derks, Terry G. J.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: John Wiley & Sons, Inc. 2020
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7383479/
https://ncbi.nlm.nih.gov/pubmed/32064649
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12224
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