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Histone acetyltransferase inhibition rescues differentiation of emerin-deficient myogenic progenitors

INTRODUCTION: Emery-Dreifuss muscular dystrophy (EDMD) is a disease characterized by skeletal muscle wasting, major tendon contractures, and cardiac conduction defects. Mutations in the gene encoding emerin cause EDMD1. Our previous studies suggested that emerin activation of histone deacetylase 3 (...

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Dettagli Bibliografici
Pubblicato in:Muscle Nerve
Autori principali: Bossone, Katherine A., Ellis, Joseph A., Holaska, James M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7382944/
https://ncbi.nlm.nih.gov/pubmed/32304242
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mus.26892
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