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The m.9143T>C Variant: Recurrent Infections and Immunodeficiency as an Extension of the Phenotypic Spectrum in MT-ATP6 Mutations?

Pathogenic variants in the MT-ATP6 are a well-known cause for maternally inherited mitochondrial disorders associated with a wide range of clinical phenotypes. Here, we present a 31- year old female with insulin-dependent diabetes mellitus, recurrent lactic acidosis and ketoacidosis recurrent infect...

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Detalhes bibliográficos
Publicado no:Diseases
Main Authors: Lehmann Urban, Diana, Motlagh Scholle, Leila, Wagner, Matias, Ludolph, Albert C., Rosenbohm, Angela
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7348873/
https://ncbi.nlm.nih.gov/pubmed/32527054
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/diseases8020019
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