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Diseases Associated with Defects in tRNA CCA Addition

tRNA nucleotidyl transferase 1 (TRNT1) is an essential enzyme catalyzing the addition of terminal cytosine-cytosine-adenosine (CCA) trinucleotides to all mature tRNAs, which is necessary for aminoacylation. It was recently discovered that partial loss-of-function mutations in TRNT1 are associated wi...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Slade, Angelo, Kattini, Ribal, Campbell, Chloe, Holcik, Martin
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7312816/
https://ncbi.nlm.nih.gov/pubmed/32471101
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21113780
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