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Severe primary refractory thrombotic thrombocytopenic purpura (TTP) in the post plasma exchange (PEX) and rituximab era

Acute acquired thrombotic thrombocytopenic purpura (TTP) requires prompt recognition and initiation of plasma exchange (PEX) therapy and immunosuppression. When PEX fails, mortality nears 100%, making finding an effective treatment crucial. Primary refractory TTP occurs when initial therapies fail o...

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Detalhes bibliográficos
Publicado no:BMJ Case Rep
Main Authors: Goranta, Sowmya, Deliwala, Smit S, Haykal, Tarek, Bachuwa, Ghassan
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7295375/
https://ncbi.nlm.nih.gov/pubmed/32532908
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2019-234091
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