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Severe primary refractory thrombotic thrombocytopenic purpura (TTP) in the post plasma exchange (PEX) and rituximab era

Acute acquired thrombotic thrombocytopenic purpura (TTP) requires prompt recognition and initiation of plasma exchange (PEX) therapy and immunosuppression. When PEX fails, mortality nears 100%, making finding an effective treatment crucial. Primary refractory TTP occurs when initial therapies fail o...

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Dettagli Bibliografici
Pubblicato in:BMJ Case Rep
Autori principali: Goranta, Sowmya, Deliwala, Smit S, Haykal, Tarek, Bachuwa, Ghassan
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Publishing Group 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7295375/
https://ncbi.nlm.nih.gov/pubmed/32532908
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2019-234091
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