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Family Studies of WHIM Syndrome

PURPOSE OF THE REVIEW: WHIM syndrome (warts, hypogammaglobulinemia, immunodeficiency, myelokathexis, or WHIMs) is a very rare autosomal dominant immunodeficiency disorder attributable to mutations in CXCR4. We reviewed clinical manifestations in 24 patients in 9 families to expand understanding of t...

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Publicado en:Curr Opin Hematol
Main Authors: Dale, David C., Dick, Emily, Kelley, Merideth, Makaryan, Vahagn, Connelly, Jim, Bolyard, Audrey Anna
Formato: Artigo
Idioma:Inglês
Publicado: 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7241424/
https://ncbi.nlm.nih.gov/pubmed/31652152
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MOH.0000000000000554
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