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Large Neutral Amino Acids (LNAAs) Supplementation Improves Neuropsychological Performances in Adult Patients with Phenylketonuria

Phenylketonuria is an inborn error of phenylalanine (Phe) metabolism diagnosed by newborn screening and treated early with diet. Although diet prevents intellectual disability, patients often show impairment of executive functions, working memory, sustained attention, and cognitive flexibility. Larg...

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Detalhes bibliográficos
Publicado no:Nutrients
Main Authors: Scala, Iris, Riccio, Maria Pia, Marino, Maria, Bravaccio, Carmela, Parenti, Giancarlo, Strisciuglio, Pietro
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7230959/
https://ncbi.nlm.nih.gov/pubmed/32326614
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu12041092
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