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Impaired regulation of KCC2 phosphorylation leads to neuronal network dysfunction and neurodevelopmental pathology

KCC2 is a vital neuronal K(+)/Cl(−) co-transporter that is implicated in the etiology of numerous neurological diseases. In normal cells, KCC2 undergoes developmental dephosphorylation at Thr(906) and Thr(1007). We engineered mice with heterozygous phospho-mimetic mutations T906E and T1007E (KCC2(E/...

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Dettagli Bibliografici
Pubblicato in:Sci Signal
Autori principali: Pisella, Lucie I., Gaiarsa, Jean-Luc, Diabira, Diabé, Zhang, Jinwei, Khalilov, Ilgam, Duan, JingJing, Kahle, Kristopher T., Medina, Igor
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7192243/
https://ncbi.nlm.nih.gov/pubmed/31615899
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1126/scisignal.aay0300
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