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Neonatal Nonketotic Hyperglycinemia: A Rare Case from Pakistan

Nonketotic hyperglycinemia (NKH) is an autosomal recessive disorder caused by a defect in glycine cleavage enzyme. It leads to the accumulation of glycine in the body tissues, blood, and cerebrospinal fluid (CSF). Most NKH cases are diagnosed during the natal period of life and are fatal if not prom...

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Dettagli Bibliografici
Pubblicato in:Cureus
Autori principali: Bin Arif, Taha, Ahmed, Jawad, Malik, Farheen, Nasir, Sharmeen, Khan, Taj M
Natura: Artigo
Lingua:Inglês
Pubblicazione: Cureus 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7145377/
https://ncbi.nlm.nih.gov/pubmed/32280576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7759/cureus.7235
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