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Hereditary and acquired angioedema: Problems and progress: Proceedings of the third C1 esterase inhibitor deficiency workshop and beyond

Hereditary angioedema (HAE), a rare but life-threatening condition, manifests as acute attacks of facial, laryngeal, genital, or peripheral swelling or abdominal pain secondary to intra-abdominal edema. Resulting from mutations affecting C1 esterase inhibitor (C1-INH), inhibitor of the first complem...

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Veröffentlicht in:J Allergy Clin Immunol
Hauptverfasser: Agostoni, Angelo, Aygören-Pürsün, Emel, Binkley, Karen E., Blanch, Alvaro, Bork, Konrad, Bouillet, Laurence, Bucher, Christoph, Castaldo, Anthony J, Cicardi, Marco, Davis, Alvin E, De Carolis, Caterina, Drouet, Christian, Duponchel, Christiane, Farkas, Henriette, Fáy, Kálmán, Fekete, Béla, Fischer, Bettina, Fontana, Luigi, Füst, George, Giacomelli, Roberto, Gröner, Albrecht, Erik Hack, C., Harmat, George, Jakenfelds, John, Juers, Mathias, Kalmár, Lajos, Kaposi, Pál N., Karádi, István, Kitzinger, Arianna, Kollár, Tímea, Kreuz, Wolfhart, Lakatos, Peter, Longhurst, Hilary J., Lopez-Trascasa, Margarita, Martinez-Saguer, Inmaculada, Monnier, Nicole, Nagy, István, Németh, Éva, Nielsen, Erik Waage, Nuijens, Jan H., O'Grady, Caroline, Pappalardo, Emanuela, Penna, Vincenzo, Perricone, Carlo, Perricone, Roberto, Rauch, Ursula, Roche, Olga, Rusicke, Eva, Späth, Peter J, Szendei, George, Takács, Edit, Tordai, Attila, Truedsson, Lennart, Varga, Lilian, Visy, Beáta, Williams, Kayla, Zanichelli, Andrea, Zingale, Lorenza
Format: Artigo
Sprache:Inglês
Veröffentlicht: American Academy of Allergy, Asthma and Immunology. Published by Mosby, Inc. 2004
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Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC7119155/
https://ncbi.nlm.nih.gov/pubmed/15356535
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jaci.2004.06.047
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