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Paroxysmal Nocturnal Hemoglobinuria: An Underestimated Cause of Pediatric Thromboembolism
Paroxysmal nocturnal hemoglobinuria (PNH) is a chronic disease caused by complement-mediated hemolysis. Clinical symptoms include intravascular hemolysis, nocturnal hemoglobinuria, thromboses, cytopenia, fatigue, abdominal pain, and a strong tendency toward bone marrow failure. It is a rare disease,...
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| Publicado en: | TH Open |
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| Main Authors: | , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado: |
Georg Thieme Verlag KG
2020
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| Acceso en liña: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7032970/ https://ncbi.nlm.nih.gov/pubmed/32090191 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0040-1702155 |
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