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GBT440 IMPROVES RED BLOOD CELL DEFORMABILITY AND REDUCES VISCOSITY OF SICKLE CELL BLOOD UNDER DEOXYGENATED CONDITIONS

BACKGROUND: In sickle cell disease (SCD), polymerization of hemoglobin S (HbS) leads to the formation of rigid, non-deformable sickled RBCs. Loss of RBC deformability, sickling and irreversible membrane damage causes abnormal blood rheology, and increases viscosity which contributes to vasoocclusion...

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Vydáno v:Clin Hemorheol Microcirc
Hlavní autoři: Dufu, Kobina, Patel, Mira, Oksenberg, Donna, Cabrales, Pedro
Médium: Artigo
Jazyk:Inglês
Vydáno: 2018
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6996409/
https://ncbi.nlm.nih.gov/pubmed/29660913
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/CH-170340
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