A carregar...

Oral administration of a synthetic vinyl-ether plasmalogen normalizes open field activity in a mouse model of rhizomelic chondrodysplasia punctata

Rhizomelic chondrodysplasia punctata (RCDP) is a rare genetic disorder caused by mutations in peroxisomal genes essential for plasmalogen biosynthesis. Plasmalogens are a class of membrane glycerophospholipids containing a vinyl-ether-linked fatty alcohol at the sn-1 position that affect functions i...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Dis Model Mech
Main Authors: Fallatah, Wedad, Smith, Tara, Cui, Wei, Jayasinghe, Dushmanthi, Di Pietro, Erminia, Ritchie, Shawn A., Braverman, Nancy
Formato: Artigo
Idioma:Inglês
Publicado em: The Company of Biologists Ltd 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6994958/
https://ncbi.nlm.nih.gov/pubmed/31862688
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.042499
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!