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Autosomal dominant Alport syndrome due to a COL4A4 mutation with an additional ESPN variant detected by whole-exome analysis

Alport syndrome (AS) is a rare hereditary disease that presents with chronic kidney disease and sensorineural hearing loss, and is diagnosed by its clinical features, pathological features on renal tissue, and mode of inheritance. We report a woman in her 20 s who exhibited persistent haematuria wit...

Πλήρης περιγραφή

Αποθηκεύτηκε σε:
Λεπτομέρειες βιβλιογραφικής εγγραφής
Τόπος έκδοσης:CEN Case Rep
Κύριοι συγγραφείς: Izumi, Yuichiro, Hamaguchi, Ami, Miura, Rei, Nakagawa, Terumasa, Nakagawa, Miyuki, Saida, Ken, Miyake, Noriko, Nagayoshi, Yu, Kakizoe, Yutaka, Miyoshi, Taku, Kohda, Yukimasa, Misumi, Yohei, Matsumoto, Naomichi, Ando, Yukio, Mukoyama, Masashi
Μορφή: Artigo
Γλώσσα:Inglês
Έκδοση: Springer Singapore 2019
Θέματα:
Διαθέσιμο Online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6990314/
https://ncbi.nlm.nih.gov/pubmed/31677115
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13730-019-00429-w
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