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A case of female Fabry disease revealed by renal biopsy

Fabry disease (FD) is an X-linked inherited glycosphingolipid metabolism disorder, therefore, heterozygous female FD patients display highly variable clinical symptoms, disease severity, and pathological findings. This makes it very challenging to diagnosing female patients with FD. A 69-year-old Ja...

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Detalhes bibliográficos
Publicado no:CEN Case Rep
Main Authors: Aratani, Sae, Yamakawa, Hiroyuki, Suzuki, Shinya, Otsuka, Tomoyuki, Sakai, Yukinao, Shimizu, Akira, Tsuruoka, Shuichi
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Singapore 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6990169/
https://ncbi.nlm.nih.gov/pubmed/31542871
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13730-019-00420-5
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