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Early Sirolimus Gel Treatment May Diminish Angiofibromas and Prevent Angiofibroma Recurrence in Children With Tuberous Sclerosis Complex

Introduction: Tuberous sclerosis complex (TSC) is a multisystem neurocutaneous disorder. Angiofibromas (AF), fibrous plaques, and hypopigmented macules are the major skin findings in TSC. Topical sirolimus reduces the volume and redness of AF and other skin findings. However, the efficacy of early i...

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Dettagli Bibliografici
Pubblicato in:Front Med (Lausanne)
Autori principali: Okanishi, Tohru, Fujimoto, Ayataka, Enoki, Hideo, Ogai, Masaaki
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6987392/
https://ncbi.nlm.nih.gov/pubmed/32039222
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fmed.2020.00001
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