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Mitochondrial Dynamics of Proximal Tubular Epithelial Cells in Nephropathic Cystinosis

Nephropathic cystinosis is a rare lysosomal storage disorder caused by mutations in CTNS gene leading to Fanconi syndrome. Independent studies reported defective clearance of damaged mitochondria and mitochondrial fragmentation in cystinosis. Proteins involved in the mitochondrial dynamics and the m...

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Détails bibliographiques
Publié dans:Int J Mol Sci
Auteurs principaux: De Rasmo, Domenico, Signorile, Anna, De Leo, Ester, Polishchuk, Elena V., Ferretta, Anna, Raso, Roberto, Russo, Silvia, Polishchuk, Roman, Emma, Francesco, Bellomo, Francesco
Format: Artigo
Langue:Inglês
Publié: MDPI 2019
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6982165/
https://ncbi.nlm.nih.gov/pubmed/31888107
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21010192
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