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Reduced FXR Target Gene Expression in Copper-Laden Livers of COMMD1-Deficient Dogs

Wilson’s disease (WD), an autosomal recessive disorder, results in copper accumulation in the liver as a consequence of mutations in the gene ATPase copper transporting beta (ATP7B). The disease is characterized by chronic hepatitis, eventually resulting in liver cirrhosis. Recent studies have shown...

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Detaylı Bibliyografya
Yayımlandı:Vet Sci
Asıl Yazarlar: Wu, Xiaoyan, Chien, Hsiaotzu, van Wolferen, Monique E., Kruitwagen, Hedwig S., Oosterhoff, Loes A., Penning, Louis C.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: MDPI 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6958483/
https://ncbi.nlm.nih.gov/pubmed/31574998
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/vetsci6040078
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