Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingolipid accumula...

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Publicado en:Circ Cardiovasc Imaging
Main Authors: Nordin, Sabrina, Kozor, Rebecca, Vijapurapu, Ravi, Augusto, João B., Knott, Kristopher D., Captur, Gabriella, Treibel, Thomas A., Ramaswami, Uma, Tchan, Michel, Geberhiwot, Tarekegn, Steeds, Richard P., Hughes, Derralynn A., Moon, James C.
Formato: Artigo
Idioma:Inglês
Publicado: Lippincott Williams & Wilkins 2019
Assuntos:
Original Articles
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6924943/
https://ncbi.nlm.nih.gov/pubmed/31826677
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCIMAGING.119.009430
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