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Study of indications for cardiac device implantation and utilisation in Fabry cardiomyopathy

BACKGROUND: Fabry disease is a treatable X-linked condition leading to progressive cardiomyopathy, arrhythmia and premature death. Atrial and ventricular arrhythmias contribute significantly to adverse prognosis; however, guidance to determine which patients require cardiovascular implantable electr...

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Detalhes bibliográficos
Publicado no:Heart
Main Authors: Vijapurapu, Ravi, Geberhiwot, Tarekegn, Jovanovic, Ana, Baig, Shanat, Nordin, Sabrina, Kozor, Rebecca, Leyva, Francisco, Kotecha, Dipak, Wheeldon, Nigel, Deegan, Patrick, Rusk, Rosemary A, Moon, James C, Hughes, Derralynn A, Woolfson, Peter, Steeds, Richard P
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6900228/
https://ncbi.nlm.nih.gov/pubmed/31446426
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/heartjnl-2019-315229
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