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Liver transplantation in a patient with hereditary haemorrhagic telangiectasia and pulmonary hypertension

Hereditary haemorrhagic telangiectasia or Rendu-Osler-Weber syndrome is a systemic vascular disease with autosomal dominant inheritance, mucocutaneous telangiectasia, and repeated nasal bleeding due to vascular abnormalities. Hereditary haemorrhagic telangiectasia may occasionally lead to complicati...

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Detalhes bibliográficos
Publicado no:Pulm Circ
Main Authors: Ejiri, Kentaro, Akagi, Satoshi, Nakamura, Kazufumi, Amioka, Naofumi, Ichikawa, Keishi, Yagi, Takahito, Ito, Hiroshi
Formato: Artigo
Idioma:Inglês
Publicado em: SAGE Publications 2019
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6923528/
https://ncbi.nlm.nih.gov/pubmed/31903186
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/2045894019896677
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