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Pulmonary hypertension in hereditary haemorrhagic telangiectasia

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant inherited disorder characterised by vascular malformations in predominantly the brain, liver and lungs. Pulmonary hypertension (PH) is increasingly recognised as a severe complication of HHT. PH may be categorised into two distinc...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:World J Cardiol
Egile Nagusiak: Vorselaars, Veronique MM, Velthuis, Sebastiaan, Snijder, Repke J, Vos, Jan Albert, Mager, Johannes J, Post, Martijn C
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Baishideng Publishing Group Inc 2015
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4438464/
https://ncbi.nlm.nih.gov/pubmed/26015855
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4330/wjc.v7.i5.230
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