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An Intriguing Involvement of Mitochondria in Cystic Fibrosis

Cystic fibrosis (CF) occurs when the cystic fibrosis transmembrane conductance regulator (CFTR) protein is not synthetized and folded correctly. The CFTR protein helps to maintain the balance of salt and water on many body surfaces, such as the lung surface. When the protein is not working correctly...

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Dades bibliogràfiques
Publicat a:J Clin Med
Autors principals: Favia, Maria, de Bari, Lidia, Bobba, Antonella, Atlante, Anna
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6912654/
https://ncbi.nlm.nih.gov/pubmed/31698802
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/jcm8111890
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