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Increased Muscleblind levels by chloroquine treatment improve myotonic dystrophy type 1 phenotypes in in vitro and in vivo models

Myotonic dystrophy type 1 (DM1) is a life-threatening and chronically debilitating neuromuscular disease caused by the expansion of a CTG trinucleotide repeat in the 3′ UTR of the DMPK gene. The mutant RNA forms insoluble structures capable of sequestering RNA binding proteins of the Muscleblind-lik...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Proc Natl Acad Sci U S A
Egile Nagusiak: Bargiela, Ariadna, Sabater-Arcis, Maria, Espinosa-Espinosa, Jorge, Zulaica, Miren, Lopez de Munain, Adolfo, Artero, Ruben
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: National Academy of Sciences 2019
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6911202/
https://ncbi.nlm.nih.gov/pubmed/31754023
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1820297116
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