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Understanding Adherence to Noninvasive Ventilation in Youth with Duchenne Muscular Dystrophy

Duchenne muscular dystrophy (DMD) is an X-linked, progressive neuromuscular disorder that results in chronic respiratory insufficiency and subsequently failure requiring non-invasive ventilation (NIV). Adherence to NIV in neuromuscular disorders and related barriers are poorly described. The aim of...

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Publicado en:Pediatr Pulmonol
Main Authors: Pascoe, John E., Sawnani, Hemant, Hater, Brooke, Sketch, Mark, Modi, Avani C.
Formato: Artigo
Idioma:Inglês
Publicado: 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6851431/
https://ncbi.nlm.nih.gov/pubmed/31475475
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ppul.24484
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